Displasia septo-óptica: hallazgos imagenológicos y revisión de tema
DOI:
https://doi.org/10.53903/01212095.125Palabras clave:
Displasia septo-óptica, Imagen por resonancia magnética, RadiologíaResumen
La displasia septo-óptica, también conocida como síndrome de De Morsier, es una enfermedad congénita que consiste en una combinación variable de defectos en su presentación clínica e imagenológica. Todos los pacientes con hipoplasia del nervio óptico deben ser estudiados imagenológicamente, en especial con resonancia magnética, con el objetivo de detectar anomalías en el desarrollo de las estructuras de la línea media del sistema nervioso central. Se realizó una revisión de la literatura y una evaluación retrospectiva de los pacientes de nuestra institución, con el fin de ilustrar los principales hallazgos neurorradiológicos de este síndrome.
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